OrphanAnesthesia
S.E. George
Klippel-Trénaunay syndrome
Klippel-Trénaunay syndrome
Schlüsselwörter
Klippel-Trénaunay syndrome; ICD 10: Q87.2; Angio osteohypertrophy, naevus vasculosus osteohypertrophicus, capillary lymphatic venous malformation (CLVM)
Keywords
Klippel-Trénaunay syndrome; ICD 10: Q87.2; Angio osteohypertrophy, naevus vasculosus osteohypertrophicus, capillary lymphatic venous malformation (CLVM)
Zusammenfassung
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Summary
Klippel-Trénaunay syndrome is a rare congenital malformation with an incidence of 1 out of 27,500 live births, characterised by a triad of venous malformations or varicose veins, cutaneous capillary malformations and bony or soft-tissue hypertrophy in affected limbs. The lung, trunk, gastrointestinal tract, neurovascular structures and the bladder may be involved with the presence of vascular malformations.