Klippel-Trén unay syndrome is a rare congenital malformation with an incidence of 1 out of 27,500 live births, characterized by a triad of venous malformations or varicose veins, cutaneous capillary malformations and bony or soft tissue hypertrophy in affected limbs. The lung, trunk, gastrointestinal tract, neurovascular structures and the bladder may be involved with the presence of vascular malformations.